Polyarteritis Nodosa and
Allied Conditions

• Polyarteritis nodosa (PN, PAN) 446.0
  • including disseminated necrotizing periarteritis, necrotizing angiitis, panarteritis nodosa, periarteritis nodosa
• Acute febrile mucocutaneous lymph node syndrome 446.1
  • including Kawasaki disease
• Hypersensitivity angiitis
• Lethal midline granuloma 446.3
  • including malignant granuloma of face
• Wegener's granulomatosis 446.4
  • including necrotizing respiratory granulomatosis, Wegener's syndrome, Churg-Strauss syndrome
• Giant cell arteritis (GCA) 446.5
  • including temporal arteritis (TA), cranial arteritis, Horton's disease
• Thrombotic microangiopathy (TMA) 446.6
  • including Moschcowitz's syndrome, thrombotic thrombocytopenic purpura (TTP)
• Takayasu's disease 446.7
  • including aortic arch arteritis, pulseless disease